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多系统萎缩合并慢性呼吸衰竭1例
引用本文:崔丽,徐先荣,王铃,王莞尔,张波,郑军,刘红巾,熊巍,付兆君. 多系统萎缩合并慢性呼吸衰竭1例[J]. 军医进修学院学报, 2010, 31(2): 127-128,147
作者姓名:崔丽  徐先荣  王铃  王莞尔  张波  郑军  刘红巾  熊巍  付兆君
作者单位:1. 空军总医院,全军临床航空医学中心,北京100142
2. 空军总医院,睡眠中心,北京100142
3. 空军总医院,呼吸内科,北京100142
摘    要:目的探讨多系统萎缩临床表现。方法分析1例晕厥主诉伴有括约肌功能障碍飞行人员临床诊治经过:并进行相关文献复习。结果依据植物神经系统衰竭、小脑损害及锥体系受损表现,临床诊断为多系统萎缩的Shy-Drager综合征亚型;同时患者存在缺氧、二氧化碳潴留、睡眠呼吸紊乱等慢性呼吸衰竭的表现。结论多系统萎缩早期病变累及脑干呼吸调节中枢,可能出现低氧、二氧化碳潴留及夜间睡眠呼吸紊乱的表现.

关 键 词:多系统萎缩  呼吸功能不全  飞行人员

A case of multiple system atrophy complicating with chronic respiratory failure
CUI Li,XU Xian-rong,WANG Ling,WANG Wan-er,ZHANG Bo,ZHENG Jun,LIU Hong-jin,XIONG Wei,FU Zhao-jun. A case of multiple system atrophy complicating with chronic respiratory failure[J]. Academic Journal of Pla Postgraduate Medical School, 2010, 31(2): 127-128,147
Authors:CUI Li  XU Xian-rong  WANG Ling  WANG Wan-er  ZHANG Bo  ZHENG Jun  LIU Hong-jin  XIONG Wei  FU Zhao-jun
Affiliation:CUI Li1,XU Xian-rong1,WANG Ling1,WANG Wan-er2,ZHANG Bo3,ZHENG Jun1,LIU Hong-jin1,XIONG Wei1,FU Zhao-jun1 1Center of Clinical Aviation Medicine,2Center of Sleep Disorder,3Department of Respiratory Diseases General Hospital of Air Force,Beijing 100142,China
Abstract:Objective To study the clinical manifestations of multiple system atrophy.Methods Clinical diagnosis of syncope complicated by sphincter dysfunction in a pilot was analyzed and its related literature was reviewed.Results The patient was diagnosed as subtype Shy-Drager syndrome,a multiple system atrophy,according to vegetative nervous system failure,lesions of cerebellum and vertebral body.The patient also had manifestations of chronic respiratory failure,such as hypoxia,carbon dioxide retention and sleep-re...
Keywords:Multiple System Atrophy  Respiratory Insufficiency  Pilots  
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