Arthrogryposis as a possible mechanism of scrotoschisis acquired in utero

A congenital defect of the scrotal wall with consequent testicular exstrophy is an exceptional finding. The etiopathogenesis of this defect is debated. We report a newborn male with arthrogryposis who presented with an exstrophied testicle. The association of these two conditions seems to establish a cause-effect relationship mediated by mechanical factors, i.e., in utero compression of the scrotum by the feet. It is likely that a similar mechanism could also be advocated to explain the previous cases reported in the literature.