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儿童遗传性心律失常的诊治进展
引用本文:冯琳,张秀芳.儿童遗传性心律失常的诊治进展[J].临床荟萃,2019,34(3):207.
作者姓名:冯琳  张秀芳
作者单位:1.河北医科大学第二医院 儿科,河北 石家庄 050000;2.厦门大学附属翔安医院 儿科,福建 厦门 361100
摘    要:回顾在遗传性心律失常领域最新发表的相关研究,主要关注与儿童心源性猝死关系密切的离子通道病,包括长QT综合征(LQTS)、短QT综合征(SQTS)、Brugada综合征(BrS)和儿茶酚胺敏感性多形性室性心动过速(CPVT),总结它们在发病机制及诊治方面的进展。

关 键 词:心律失常     心性    Brugada综合征  心动过速     室性  猝死     心脏  婴儿猝死  

Progress of inherited arrhythmia in children
Feng Lin,Zhang Xiufang.Progress of inherited arrhythmia in children[J].Clinical Focus,2019,34(3):207.
Authors:Feng Lin  Zhang Xiufang
Affiliation:1.Department of Pediatric,  the Second Hospital of Hebei Medical University, Shijiazhuang 050000, China; 2.Department of Pediatric,Xiang'anHospital of Xiamen University, Xiamen 361100, China
Abstract:Recent and relevant research published in the field of inherited arrhymias were reviewed, focusing on the 'channelopathies' that are associated with sudden cardiac death (SCD) in children, including long QT syndrome (LQTS), short QT syndrome (SQTS), Brugada syndrome(BrS), and catecholaminergic polymorphic ventricular tachycardia (CPVT).
Keywords:arrhythmias     cardiac  brugada syndrome     tachycardia     ventricular  death     sudden     cardiac  sudden infant death  
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