排序方式: 共有32条查询结果,搜索用时 15 毫秒
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目的 探讨先天性皮肤缺损的病因、分类、治疗及预后,提高该病的诊治水平.方法 回顾性分析我院治疗的3例先天性皮肤缺损患儿发病特点、治疗过程、方法,并复习国内外文献中报道的皮肤缺损305例,总结先天性皮肤缺损的临床特点及诊治经验.结果 3例患儿缺损皮肤均由羊皮纸样瘢痕组织愈合,无组织挛缩,无活动障碍.305例患儿中死亡8例;保守治疗234例;手术治疗63例,其中因瘢痕挛缩影响肢体功能者5例.该病致死率、致残率低,预后良好.结论 先天性皮肤缺损是一种病因尚不明确的疾病,创面表浅者多可经保守治疗后痊愈,骨外露、重要脏器外露、深度缺损宜适时采用手术治疗,该疾病若能给予正确处理,预后良好,对患儿日常生活影响小. 相似文献
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目的探讨经肛穴肛门直肠成形术在女婴先天性肛门闭锁并直肠前庭瘘中的临床疗效。方法回顾性分析2012年7月至2022年7月郑州大学第一附属医院小儿外科收治的69例肛门闭锁并直肠前庭瘘女婴的临床资料, 根据手术方式将患儿分为2组:行经肛穴肛门直肠成形术者34例(A组);行前矢状入路肛门直肠成形术者35例(B组)。比较2组手术时间、住院时间及近期并发症、远期并发症和排便功能(术后6个月Rintala评分)情况。术后并发症发生率采用χ2检验比较;手术时间、术后住院时间及术后6个月Rintala评分采用配对t检验比较。结果 A组手术时间[(80.18±9.29) min]及术后住院时间[(6.10±1.52) d]均短于B组[(103.85±8.26) min、(7.63±2.40) d], 差异均有统计学意义(t=11.40、2.62, 均P<0.05);术后6个月排便功能Rintala评分总分A组[(19.36±0.93)分]较B组[(18.76±0.44)分]高, 差异有统计学意义(t=3.20, P<0.05)。近期并发症:A组4/34例(11.8%), B组7/35例(20.... 相似文献
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患儿,男,2岁8个月,因咽后壁脓肿引流术及气管切开术后5个月,拔管困难4个月人院.5个月前,患儿因喘鸣进行性加重2年,呼吸困难1d入住耳鼻喉科,查CT见右侧咽后壁囊性肿物,急诊行气管切开及脓肿切开引流术,术后呼吸困难解除,带气管套管出院.4个月前拟行拔管,拔管后出现呼吸困难未予拔除. 相似文献
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目的 探讨小儿肝母细胞瘤累及肝内重要血管术中处理方法及其疗效.方法 对2005年4月至2008年8月25例小儿肝母细胞瘤切除术中对累及肝内重要血管的具体处理方法进行分析,按术中受累血管处理不同分为2组,血管结扎组10例、血管修补组15例,血管结扎组:累及的肝内重要血管连同瘤体、受累肝叶/肝实质一并结扎切除;血管修补组:对受累肝内重要血管分离,尽可能保留受累肝内重要血管及所支配之正常肝叶/实质.结合术后随访情况分析疗效.结果 血管结扎组中放弃手术1例,姑息性切除3例,完整切除6例,术后肝功能衰竭死亡2例,痊愈出院4例;血管修补组均完整切除痊愈出院.随访5~36个月(中位随访时间20个月),血管结扎组生存1例,血管修补组生存11例.结论 辅以血管修补的肿块切除术可扩大肝母细胞瘤手术适应证,有效预防术后肝功能衰竭,安全度过围手术期,为早期化疗提供时机. 相似文献
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目的:基于网络药理学探讨四神煎治疗类风湿关节炎(rheumatoid arthritis, RA)的作用机制。方法:通过中药系统药理数据库和分析平台(traditional chinese medicine systems pharmacology database and analysis platform, TCMSP)、中医药百科全书数据库(encyclopedia of traditional chinese medicine, ETCM)检索四神煎组方中药的主要化学成分,并结合文献进行筛选、补充;通过Pubchem有机小分子生物活性数据库检索化学成分的SMILES结构式及2D结构,经Swiss ADME数据库筛选后将符合标准的化学成分上传至Swiss Target Prediction数据库预测药物活性靶点;通过人类基因数据库(Gencards)、在线人类孟德尔遗传数据库(online mendelian inheritance in man, OMIM)、治疗靶标数据库(therapeutic target database, TTD)、DrugBank数据库获取RA疾病相... 相似文献
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Background: Hepatoblastoma (HB) is a rare childhood tumor. We investigated the effect of intraoperative management of the intrahepatic major vessels in children with HB.
Methods: Between April 2005 and August 2012, surgical resection was performed for 50 children with hepatoblastoma. These children were divided into a vessel-ligation group (n = 20) or a vessel-repair group (n = 30). In the vessel-ligation group, the intrahepatic major vessels were ligated and removed together with the tumor and the affected liver lobe/liver parenchyma. In the vessel-repair group, the affected intrahepatic major vessels were dissected and preserved as much as possible and the normal liver lobe/liver parenchyma and blood supply from these vessels were also preserved. The outcomes were analyzed by postoperative follow-up.
Results: In the vessel-ligation group, 2 patient gave up surgery, 6 patients underwent palliative resection, and 12 patients underwent en bloc resection; 4 patients died of liver failure and 8 patients fully recovered and were discharged. In the vessel-repair group, all 30 patients underwent en bloc resection and were discharged after satisfactory healing. After a follow-up time of 5-36 months (median: 20 months), 2 patient in the vessel-ligation group survived and 22 patients in the vessel-repair group survived.
Conclusion: Patients with HB can be successfully treated by tumor resection with vascular repair. This method prevents postoperative liver failure, ensures patient safety during the perioperative period, and allows for early chemotherapy. 相似文献