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质子磁共振波谱对线粒体脑肌病的诊断作用
引用本文:王起,戚晓昆,林伟,谢琰臣,袁云.质子磁共振波谱对线粒体脑肌病的诊断作用[J].海军总医院学报,2007,20(1):19-22.
作者姓名:王起  戚晓昆  林伟  谢琰臣  袁云
作者单位:1. 海军总医院神经内科,北京,100037
2. 海军总医院医学影像科,北京,100037
3. 北京友谊医院神经内科,北京,100050
4. 北京大学第一医院神经内科,北京,100034
摘    要:目的 探讨质子磁共振波谱在线粒体脑肌病中的特点及其诊断价值.方法 对2例临床诊断为线粒体脑肌病的患者行常规磁共振及质子磁共振波谱检查,分析其谱线特点.结果 2例患者行质子磁共振波谱检查均有明显的乳酸峰出现,1例在常规磁共振成像上显示正常的区域也有小的乳酸峰.结论 质子磁共振波谱可以早期反映线粒体脑肌病的异常代谢,有助于提高诊断的准确性.

关 键 词:线粒体脑肌病  磁共振波谱
文章编号:1009-3427(2007)01-0019-04
收稿时间:2006-12-26
修稿时间:2006年12月26

Value of Proton Magnetic Resonance Spectroscopy on the Diagnosis of Mitochondrial Encephalomyopathy
WANG Qi,QI Xiao-kun,LIN Wei,XIE Yan-chen,YUAN Yun.Value of Proton Magnetic Resonance Spectroscopy on the Diagnosis of Mitochondrial Encephalomyopathy[J].Journal of Naval General Hospital of PLA,2007,20(1):19-22.
Authors:WANG Qi  QI Xiao-kun  LIN Wei  XIE Yan-chen  YUAN Yun
Affiliation:1. Department of Neurology,Naval General Hospital,Beijing 100037, China; 2. Department of Radiology,Naval General Hospital,Beijing 100037, China; 3. Department of Neurology,Friendship Hospital, Beijing 100050, China; 4. Department of Neurology,Peking Universite First Hospital,Beijing 100034, China
Abstract:Objective To investigate the characteristics of spectra of proton magnetic resonance spectroscopy(1H-MRS) and its value in patients with mitochondrial encephalomyopathy.Methods Two clinically diagnosed patients with ME underwent conventionality MRI and 1H-MRS examination,and the characteristics of spectra were analyzed.Results Obvious lactate peaks were detected in the two patients with 1H-MRS,and small lactate peak appeared on normal area with conventional MRI in one case.Conclusion 1H-MRS may reflect the disorder of metabolism and be helpful for diagnosis.
Keywords:Mitochondrial encephalomyopathy  Magnetic resonance spectroscopy
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