| 黏多糖病患者神经系统CT及MRI表现 |
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| 引用本文： | 刘玥,曾津津,彭芸,孙国强,刘宁瑶.黏多糖病患者神经系统CT及MRI表现[J].临床放射学杂志,2008,27(12):1725-1729. |
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| 作者姓名： | 刘玥 曾津津 彭芸 孙国强 刘宁瑶 |
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| 作者单位： | 首都医科大学附属北京儿童医院影像中心,100045 |
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| 摘 要： | 目的 分析黏多糖病(mucopolysaccharidosis,MPS)患者神经系统CT和MRI表现,探讨其对MPS诊断和不同类型MPS鉴别的意义. 资料与方法 回顾性分析24例MPS患儿中枢神经系统的CT和MRI表现.11例行头颅加脊柱MRI,5例行头颅MRI,4例行CT检查,2例行头颅MRI及MRA,1例行头颅MRI及CT检查,1例行颈部MRI. 结果 Ⅰ-H型6例,Ⅰ-S型1例,Ⅱ型1例,Ⅲ型1例,Ⅳ型5例,Ⅵ型9例,Ⅶ型1例.舟状头3例,脑室扩张5例,脑萎缩4例,脑室旁脑白质、放射冠及胼胝体筛网状改变13例,室旁斑片状长T2信号11例,枕骨大孔狭窄,脊髓受压10例,其中1例髓内示异常长T2信号,双侧颞极蛛网膜囊肿3例,寰枢椎畸形7例. 结论 MPS患者中枢神经系统的CT及MRI表现有一定的特征,对临床诊断MPS和鉴别不同类型MPS有帮助.
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| 关 键 词： | 黏多糖病 体层摄影术 X线计算机 磁共振成像 |
The Manifestation of CT and MR Imaging in Central Neural System of Mucopolysaccharidosis |
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| LIU Yue,ZENG Jinjin,PENG Yun,et al..The Manifestation of CT and MR Imaging in Central Neural System of Mucopolysaccharidosis[J].Journal of Clinical Radiology,2008,27(12):1725-1729. |
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| Authors: | LIU Yue ZENG Jinjin PENG Yun |
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| Affiliation: | LIU Yue,ZENG Jinjin,PENG Yun,et al.Imaging Center,Beijing Children\'s Hospital Affiliated to Capital Medical University,Beijing 100045,P.R.China |
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| Abstract: | Objective To analyze CT and MR findings of central neural system in mucopolysaccharidosis(MPS) and to evaluate the diagnosis and differentional diagnosis value. Materials and Methods CT and MRI findings of mucopolysaccharidosis in 24 children (15 male,9 female; mean age 6.3 years,range from 7 months to 16 years) were retrospectively analyzed. 17 patients presented normal mentality, and 7 patients presented different degree of mental retardation. All patients were confirmed by skeletal X-ray examination, gen... |
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| Keywords: | Mucopolysaccharidosis Tomography X-ray computed Magnetic resonance imaging |
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